CHILDS NERVOUS SYSTEM, cilt.24, sa.1, ss.149-151, 2008 (SCI-Expanded)
Introduction Incontinentia pigmenti is a rare, X-linked dominant multisystem genodermatosis that presents at or soon after birth with characteristic cutaneous signs. The main features occur in the skin where a blistering rash occurs in the newborn period, followed by the blisters becoming raised-like warts. After the skin, the central nervous system is the next most affected system.